MUGS is a fluorogenic substrate used in the diagnosis of GM2 gangliosidoses in leukocytes. Genetic defects in human b-hexosaminidase isozymes (Hex A & Hex B) result in various clinical and biochemical types of GM2 gangliosidosis (eg. Tay Sachs disease).
Applications
Fluorogenic substrate used for the diagnosis of GM2 gangliosidoses in leukocytes
Form
Solid
CAS No.
210357-38-3
Molecular Weight
497.51
Storage
Store at -20° C
Synonyms
7-[[2-(Acetylamino)-2-deoxy-6-O-sulfo-β-D-glucopyranosyl]oxy]-4-methyl-2H-1-benzopyran-2-one Monopotassium Salt
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